Epihtelioid Sclerosing Fibrosarcoma of the Chest Wall: A Case Report and Review of the Literature

Author(s): Derqaoui Sabrine, Laraqui Yasmine, Raissouni Khouloud, Jahid Ahmed, Achir Abdellah, Bernoussi Zakia, Znati Kaoutar

Background: SEF is a rare variant of fibrosarcoma, mostly occurring in extraosseous sites. It is a clinically challenging entity as no standardized treatment regimens are available. SEF’s literature is limited, due to its rarity and recent recognition. The current study reports the case of a patient with SEF arising from the anterior chest wall.

Case Presentation: A 26-year-old man presented with a 6 years history of a left superior chest mass. Imaging revealed an invasive tumor of the right pectoral region, without metastases. The patient undergone surgical resection of the tumor. Histology and immunohistochemistry confirmed the diagnosis and revealed a hypocellular tumor with large areas of hyalinized fibrous stroma. The patient was referred to the oncology department to undergo postoperative treatment (radiotherapy/chemotherapy).