Congenital Common Bile Duct Agenesis: An Extremely Rare Anomaly - Two Case Reports and Review of Literature

Author(s): Louis F Chai, Alexander E Trebelev, Gary S Xiao

Variations of the hepatico-pancreatic-biliary system are frequently vascular, but biliary duct deviations can occur.1 In the extra-hepatic biliary system, anomalies occur during foregut development and include accessory ducts, anomalous insertions, or agenesis. Though anomalies may be clinically silent, discovery usually occurs in symptomatic patients resulting in imaging or intraoperatively during exploration. The rarest of anomalies is common bile duct agenesis, resulting in formation of a cholecystohepatic duct, gallbladder interposition, or perhaps most appropriately, a hepaticocystic duct.2-3 We present here two cases discovered intraoperatively and an updated review on this anomaly.