Extra-Renal Wilms’ Tumor in Left Lobe of Liver: A Case Report of the Rare Tumor with Review of Literature

Author(s): Ajay Krishna Boralkar, Manoj Narayanrao More, Kunal Vikram Singh, Arpita Khandelwal, Aditya Abhijeet Phadke

Wilms tumor is the commonest childhood tumor. Extra renal Wilms' tumor is a nephroblastoma arising in locations other than kidneys. The tumor arises from misplaced metanephric blastema or is contemplated to arise from pluriotent cells. A metstasis, origin of tumor in kidneys and supernumery kidneys have to be ruled out to assign a diagnosis of extrarenal Wilms' tumor. It has been commonly reported to occur in retroperitoneum but also in inguinal region, pelvis, testis and colon. The age of occurence has been reported as Wilms; tumor in literature. It is mostly diagnosed post operatively. A preoperative biopsy combined with immunohistochemistry can help in diagnosing tumors in cases where neoadjuvant chemotherapy is anticipated. The WIlms'tumors in extrarenal location largely have favourable histology and are treated on same guidelines as Wilms' tumor. Here we present a case of extra renal Wilms' tumor arising in left lobe of liver. Liver as location for an extra renal Wilms' tumor was not found in literature.